National Acoustic Laboratories Library

The management of pediatric hearing loss caused by auditory neuropathy spectrum disorder (Record no. 2844)

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control field 20180202143832.0
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Transcribing agency National Acoustics Laboratories
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Personal name Pham, Nguyen S
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Title The management of pediatric hearing loss caused by auditory neuropathy spectrum disorder
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Summary, etc Purpose of review<br/>Auditory neuropathy spectrum disorder (ANSD) is a condition in which auditory testing reveals normal<br/>otoacoustic emissions, but auditory brainstem testing is abnormal or absent and speech discrimination is<br/>poor. This constellation of findings ostensibly suggests that the cochlea is healthy and an abnormality of<br/>conduction or processing of sound occurs along the nerve fibers. As more is learned about this condition, it<br/>is becoming clear that ANSD describes heterogeneous, distinct clinical entities that must be taken into<br/>account when devising treatment modalities.<br/>Recent findings<br/>Modern auditory testing, genetic testing, and neuroimaging can allow for an accurate understanding of the<br/>location of the lesion causing ANSD in the auditory pathway. Contributing causes can include genetic<br/>mutations, absent or deficient cochlear nerve, hypoxia and jaundice among others. Hearing aids can be<br/>successful in the management of ANSD. Several studies suggest that cochlear implantation can lead to<br/>successful hearing outcomes in a subset of this patient population.<br/>Summary<br/>Auditory neuropathy spectrum disorder represents a relatively rare but important diagnosis for clinicians.<br/>Treatment for this condition includes hearing aids and FM systems in more mild cases, and cochlear<br/>implants in severe cases. Cochlear implantation for many patients can lead to a good hearing outcomes<br/>but the outcome can vary greatly depending on the underlying etiology of ANSD.<br/>Keywords<br/>auditory nerve dys-synchrony, auditory neuropathy spectrum disorder, cochlear implantation, sensorineural<br/>hearing loss
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Topical term or geographic name as entry element Auditory nerve dyssynchrony|
650 ## - SUBJECT ADDED ENTRY--TOPICAL TERM
Topical term or geographic name as entry element Auditory neuropathy spectrum disorder
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Topical term or geographic name as entry element Cochlear implantation
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Topical term or geographic name as entry element Sensorineural hearing loss
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Relationship information 25 (5) p. 396-399 (October 2017)
Title Current Opinion in Otolaryngology & Head and Neck Surgery
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Uniform Resource Identifier <a href="https://dspace.nal.gov.au/xmlui/bitstream/handle/123456789/785/The%20management%20of%20pediatric%20hearing%20loss%20caused.pdf?sequence=1&isAllowed=y">https://dspace.nal.gov.au/xmlui/bitstream/handle/123456789/785/The%20management%20of%20pediatric%20hearing%20loss%20caused.pdf?sequence=1&isAllowed=y</a>
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Source of classification or shelving scheme Universal Decimal Classification
Koha item type Journal article

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